1 Laboratoire de Psychopathologie et Processus de Santé (LPPS), Université de Paris, Institut de Psychologie, Boulogne-Billancourt, France.
2 Service d'Addictologie, Hôpital René-Muret (AP-HP), Hôpitaux Universitaires Paris Seine-Saint-Denis (HUPSSD), Sevran, France.
3 Interpersonal Relationships and Development Laboratory, Centre for Research in Human Development, Department of Psychology, Concordia University, Montreal, QC, Canada.
4 Psychiatrie de l'Adulte et du Sujet Âgé, Hôpital Européen Georges-Pompidou, Paris, France.
5 Unité de Psycho-Oncologie, Institut Gustave Roussy, Villejuif, France.

Improved treatments for cystic fibrosis allow more patients to become parents. This article presents a systematic review of literature on cystic fibrosis patients' experience of parenthood. Five databases (Cairn, Cochrane Library, PsycINFO, PubMed and ScienceDirect) produced 2335 documents that were screened. In total, 13 documents were retained and assessed with validated criteria. Five themes related to cystic fibrosis parenthood were discovered: population presentation, health and treatment adherence, adjustments, role of professionals and pressured temporality. Parenthood requires an important reorganisation of daily life in order to remain capable of childcare. Regardless of negative health impacts, cystic fibrosis parents have a positive outlook on parenthood.